Parry Romberg Syndrome or progressive hemifacial atrophy (PHA) is an uncommon degenerative condition characterized by slowly progressive atrophy of muscles, bone and skin of the face before spontaneously entering remission. It usually involves one half. Rarely both halves of the face may be involved. The various proposed causes include cerebral disturbance of fat metabolism or a trophic malformation of the cervical sympathetic nervous system. Possible factors involved in the pathogenesis include heredity, trauma, viral infections, endocrine disturbance and autoimmunity. Differential Diagnosis include juvenile localized scleroderma, Rasmussen encephalitis, Barrarquer-Simon Syndrome, congenital hemiatrophy, primary hemifacial hypertrophy. The main aim of treatment is aesthetic restoration. There is no cure or treatment to stop the progression of the disease. We report case of Parry Romberg Syndrome who reported to the paediatric outpatient department of a peripheral hospital.