Congenital Heart Disease (CHD) comprises one of the major diseases in pediatric age group. Among the all congenital malformations, Congenital Heart Disease is leading cause of morbidity and mortality in children. Congenital heart disease is defined as structural malformation of heart or intra-thoracic great vessels present since birth that is actually or potentially of functional significance regardless of the age of detection. Hence based on above literature findings the present study was done for assessment of Incidences and risk factors of congenital heart diseases in Children of North Bihar region. The present study was done in Department of Pediatrics, Darbhanga Medical College and Hospital, Laheriasarai, Darbhanga, Bihar, India. Out of the total children referred to our hospital 50 newly diagnosed cases with the Congenital Heart Diseases were enrolled in the present study. Study group was first assessed clinically according to a preformed proforma including sex and age of presentation & undergone antenatal history, routine investigations, chest x-ray, ECG. Final diagnosis was confirmed by Echocardiography, then analysed to know pattern of congenital heart disease. The data generated from the present study concludes that Ventricular Septal defect as well as Tetralogy of Fallot is most common abnormality that needs detection of risk factors in pregnant mothers and early interventional treatments for diseases. Several antenatal factors were found to be associated with the incidence of congenital heart disease emphasizing the need to prioritize antenatal care and counselling to pregnant mothers along with good maternal nutrition and folic acid supplementation.